Dyke-Davidoff-Masson Syndrome: A Rare Presentation

Dr GURDEEP KAUR; Dr RAHUL METRI; Dr AMIT POORIA; Dr ABHINAV; Dr  RAJESH MEENA

doi:10.59793/ijcp.v34i10.854

Authors

Dr GURDEEP KAUR Senior Professor and Unit Head
Dr RAHUL METRI Room no. 525, PG’s Boys Hostel, Dilshad Bhawan, Chetak Circle, Udaipur - 313001, Rajasthan, India
Dr AMIT POORIA Junior Resident
Dr ABHINAV Junior Resident
Dr RAJESH MEENA Assistant Professor Dept. of General Medicine, RNT Medical College, Udaipur, Rajasthan, India

DOI:

https://doi.org/10.59793/ijcp.v34i10.854

Keywords:

Tonic-clonic seizures,, hemiparesis,, facial asymmetry, cerebral hemiatrophy,, homolateral hypertrophy of skull,, NCCT head

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) is characterized by seizures, facial asymmetry, contralateral
hemiplegia and mental retardation. The characteristic radiological features are cerebral hemiatrophy with homolateral
hypertrophy of skull and sinuses. Case report: We report a case of DDMS in a 41-year-old female who presented with
generalized tonic-clonic seizures, hemiparesis of the right upper and lower limb with deviation of the mouth to left.
Noncontrast computed tomography (NCCT) head and magnetic resonance imaging (MRI) revealed hemiatrophy of the right
cerebral hemisphere. Conclusion: DDMS is a rare disease; hence, diagnosing and managing such patients may be challenging.
Our aim is to draw attention of the treating physicians towards this disease with the help of this case report.